产品详情 |
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Antigenic Specificity | EVC2 |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human |
Isotype | n/a |
Format | Protein A purified |
Size | 100ul |
Concentration | 1ug/ul |
Applications | WB, IHC-P, IF(IHC-P) |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | EVC2 Polyclonal Antibody. • Target Background: EVC2 is an integral membrane protein that plays a vital role in bone formation and skeletal development. Defects in EVC2 are a cause of Ellis-van Creveld syndrome (EVC), also known as chondroectodermal dysplasia. EVC is an autosomal recessive disorder characterized by the clinical tetrad of chondrodystrophy, polydactyly, ectodermal dysplasia and cardiac anomalies. Patients manifest short-limb dwarfism, short ribs, postaxial polydactyly and dysplastic nails and teeth. Congenital heart defects, mo |
Immunogen | KLH conjugated synthetic peptide derived from human EVC2 |
Other Names | Ellis van Creveld syndrome 2; LBN; Limbin; LBN_HUMAN. |
Gene, Accession # | Gene ID: 132884 |
Catalog # | bs-6638R |
Price | |
Order / More Info | EVC2 Antibody from BIOSS ANTIBODIES |
Product Specific References | n/a |
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