| 产品详情 |
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| Antigenic Specificity | GLA |
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| Clone | 13j37 |
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| Host Species | Recombinant Mouse |
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| Reactive Species | human |
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| Isotype | IgG |
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| Format | purified |
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| Size | n/a |
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| Concentration | n/a |
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| Applications | ELISA, IC, IHC, WB |
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| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
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| Description | Mouse Anti-GLA Recombinant Antibody (13j37). This product is antibody recognizes GLA. The antibody 13j37 immunoassay techniques such as: ELISA, IC, IHC, WB. This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008] |
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| Immunogen | Recombinant protein corresponding to Met1 thru Gly80 of human GLA (UniProt accession #P06280), containing a His tag and S-tag at the N-terminus. Sequence: MHHHHHHSSG LVPRGSGMKE TAAAKFERQH MDSPDLGTDD DDKAMADIGS EF-MQLRNPELHL GCALALRFLA LVSWDIPGAR ALDNGLARTP TMGWLHWERF MCNLDCQEEP DSCISEKLFM EMAELMVSEG |
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| Other Names | Galactosidase Alpha; Alpha-D-Galactosidase A; EC 3.2.1.22; Melibiase; Alpha-D-Galactoside Galactohydrolase 1; Alpha-D-Galactoside Galactohydrolase; Alpha-Galactosidase A; |
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| Gene, Accession # | Gene ID: 2717, UniProt: P06280 |
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| Catalog # | CBMAB-G3644-LY |
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| Price | |
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| Order / More Info | GLA Antibody from CREATIVE BIOLABS |
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| Product Specific References | n/a |
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