| 产品详情 |
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| Antigenic Specificity | GALNS |
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| Clone | polyclonal |
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| Host Species | Goat |
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| Reactive Species | human |
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| Isotype | n/a |
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| Format | purified |
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| Size | 100 ug |
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| Concentration | n/a |
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| Applications | peptide-ELISA: 1:64000, Western Blot: 0.01-0.03 µg/mL |
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| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
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| Description | GALNS Polyclonal Antibody. This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder. |
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| Immunogen | n/a |
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| Other Names | GALNS; galactosamine (N-acetyl)-6-sulfate sulfatase (Morquio syndrome, mucopolysaccharidosis type IVA); GALNAC6S; GAS; MPS4A; N-acetylgalactosamine-6-sulfatase; chondroitinase |
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| Gene, Accession # | Entrez: 2588; Uniprot: P34059 |
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| Catalog # | PA5-18808 |
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| Price | |
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| Order / More Info | GALNS Antibody from INVITROGEN ANTIBODIES |
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| Product Specific References | n/a |
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