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| Product Name | Cystathionine β Synthase Activity Assay Kit (Fluorometric) |
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| Description | Cystathionine β Synthase (EC 4.2.1.22, CβS) is a PLP-dependent enzyme that catalyzes the formation of H2S and cystathionine when using cysteine and homocysteine as substrates. Known for its role in human sulfur metabolism, mutations in the gene encoding CβS can result in high concentrations of homocysteine in plasma. Elevated circulating concentrations of homocysteine result in genetic disorders including Homocysteinuria and Down syndrome. Specifically, Homocysteinuria is an autosomal recessive disease with clinical manifestations including mental retardation, thromboembolism and connective tissue defects. Hydrogen sulfide, CβS product, is an important gaseous mediator, like nitric oxide, that has significant effects on |
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| Size | 100 assays |
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| Concentration | n/a |
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| Applications | Rapid assessment of native/recombinant CβS and CβS activity in mammalian samples |
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| Other Names | n/a |
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| Gene, Accession, CAS # | n/a |
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| Catalog # | K998-100 |
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| Order / More Info | Cystathionine β Synthase Activity Assay Kit (Fluorometric) from BIOVISION, INC. |
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| Product Specific References | n/a |
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