abbexa；abx002344；1,4-α-葡聚糖支化酶（GBE1）抗体；1,4-Alpha-Glucan-Branching Enzyme (GBE1) Antibody
型号:abx002344
联系人:程园
联系电话:18611717737
品牌:abbexa
GBE1 Antibody is a Rabbit Polyclonal antibody against GBE1. The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease).
| Target | GBE1 |
| Reactivity | Human, Mouse |
| Host | Rabbit |
| Clonality | Polyclonal |
| Tested Applications | WB, IF/ICC |
| Recommended dilutions | WB: 1/1000 - 1/2000, IF/ICC: 1/20 - 1/50. Optimal dilutions/concentrations should be determined by the end user. |
| Immunogen | Recombinant protein of human GBE1. |
| Purification | Affinity purified. |
| Form | Liquid |
| Isotype | IgG |
| Conjugation | Unconjugated |
| Storage | Store at 4 °C. |
| Molecular Weight |
Calculated MW: 80 kDa Observed MW: 80 kDa |
| Swiss Prot | Q04446 |
| GeneID | 2632 |
| Gene Symbol | GBE1 |
| Concentration | > 1 mg/ml |
| Buffer | PBS, pH 7.3, 0.02% sodium azide. |
| UNSPSC Code | 12352203 |
| Availability | Shipped within 5-10 working days. |
| Note | This product is for research use only. |
GBE1抗体是抗GBE1的兔多克隆抗体。由该基因编码的蛋白质是糖原分支酶，其催化α-1,4-连接的葡糖基单元从糖原链的外端转移到相同或相邻糖原链上的α-1,6位置。链的分支对于增加糖原分子的溶解度是必要的，并因此降低细胞内的渗透压。这种酶的高水平存在于肝脏和肌肉中。该基因的突变与糖原贮积病IV（也称为安徒生病）有关。
| 目标 | GBE1 |
| 反应 | 人类，老鼠 |
| 主办 | 兔子 |
| 克隆 | 多克隆 |
| 经测试的应用程序 | WB，IF / ICC |
| 的稀释液 | WB：1/1000 - 1/2000，IF / ICC：1/20 - 1/50。佳稀释度/浓度应由终用户确定。 |
| 免疫原 | 人GBE1的重组蛋白。 |
| 纯化 | 亲和纯化。 |
| 形成 | 液体 |
| 同型 | IgG抗体 |
| 共轭 | 非结合 |
| 存储 | 储存在4°C。 |
| 分子量 |
计算的MW：80kDa 观察到的MW：80kDa |
| Swiss Prot | Q04446 |
| GeneID | 2632 |
| 基因符号 | GBE1 |
| 浓度 | > 1毫克/毫升 |
| 缓冲 | PBS，pH 7.3,0.02％叠氮化钠。 |
| UNSPSC代码 | 12352203 |
| 可用性 | 5-10个工作日内发货。 |
| 注意 | 该产品仅供研究使用。 |
