abbexa；abx034400；1,4-Alpha-Glucan-Branching Enzyme (GBE1) Antibody；1,4-α-葡聚糖支化酶（GBE1）抗体
型号:abx034400
联系人:程园
联系电话:18611717737
品牌:abbexa
GBE1 is a glycogen branching enzyme that catalyzes the transfer of alpha-1, 4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1, 6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease).
| Target | GBE1 |
| Reactivity | Human, Mouse |
| Host | Rabbit |
| Clonality | Polyclonal |
| Tested Applications | WB, IF/ICC |
| Recommended dilutions | Optimal dilutions/concentrations should be determined by the end user. |
| Immunogen | Human GBE1. |
| Purification | Peptide Affinity Purified Rabbit Polyclonal Antibody. |
| Isotype | IgG |
| Conjugation | Unconjugated |
| Specificity | This GBE1 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 527-556 amino acids from the Central region of human GBE1. |
| Storage | Aliquot and store at -20 °C. Avoid repeated freeze/thaw cycles. |
| Swiss Prot | Q04446 |
| Buffer | PBS with 0.09% (W/V) sodium azide. This antibody is purified through a protein A column, followed by peptide affinity purification. |
| UNSPSC Code | 12352203 |
| Availability | Shipped within 5-10 working days. |
| Note | This product is for research use only. |
GBE1是糖原分支酶，其催化α-1,4-连接的葡糖基单元从糖原链的外端转移到相同或相邻糖原链上的α-1,6位。链的分支对于增加糖原分子的溶解度是必要的，并因此降低细胞内的渗透压。这种酶的高水平存在于肝脏和肌肉中。该基因的突变与糖原贮积病IV（也称为安徒生病）有关。
| 目标 | GBE1 |
| 反应 | 人类，老鼠 |
| 主办 | 兔子 |
| 克隆 | 多克隆 |
| 经测试的应用程序 | WB，IF / ICC |
| 的稀释液 | 佳稀释度/浓度应由终用户确定。 |
| 免疫原 | 人类GBE1。 |
| 纯化 | 肽亲和纯化兔多克隆抗体。 |
| 同型 | IgG抗体 |
| 共轭 | 非结合 |
| te异性 | 该GBE1抗体由用来自人GBE1的中心区域的527-556个氨基酸之间的KLH缀合的合成肽免疫的兔产生。 |
| 存储 | 分装并储存在-20°C。避免反复冻/融循环。 |
| Swiss Prot | Q04446 |
| 缓冲 | 含有0.09％（W / V）叠氮化钠的PBS。通过蛋白A柱纯化该抗体，然后进行肽亲和纯化。 |
| UNSPSC代码 | 12352203 |
| 可用性 | 5-10个工作日内发货。 |
| 注意 | 该产品仅供研究使用。 |
